Pearson syndrome in a child transplanted for diamond-blackfan anemia

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dc.authoridVedat Uygun / 0000-0003-3257-7798
dc.authoridHayriye Daloğlu / 0009-0008-6996-0292
dc.authorscopusidVedat Uygun / 10043117000
dc.authorscopusidHayriye Daloğlu / 6504521157
dc.authorwosidVedat Uygun / AGH-4534-2022
dc.authorwosidHayriye Daloğlu / ESQ-7472-2022
dc.contributor.authorUygun, Vedat
dc.contributor.authorDaloğlu, Hayriye
dc.contributor.authorÖztürkmen, Seda
dc.contributor.authorKarasu, Gülsün
dc.contributor.authorYeşilipek, Akif
dc.date.accessioned2021-09-29T08:24:44Z
dc.date.available2021-09-29T08:24:44Z
dc.date.issued2021en_US
dc.departmentİstinye Üniversitesi, Tıp Fakültesi, Dahili Tıp Bilimleri Bölümüen_US
dc.description.abstractPearson syndrome (PS), shares a number of overlapping features with Diamond-Blackfan anemia (DBA), including early onset of severe anemia, making differential diagnosis important. Differential diagnosis of DBA and PS is critical, since those with DBA may respond to treatment with steroids, may undergo remission, or may benefit from hematopoietic stem cell transplantation (HSCT). However, patients with PS have a different prognosis, with a very high risk of developing acidosis, metabolic problems, and pancreatic dysfunction, and a shorter life expectancy than those with DBA. Here we present a patient who underwent HSCT for DBA but was subsequently diagnosed with PS after developing some complications.en_US
dc.identifier.citationUygun, V., Daloğlu, H., Öztürkmen, S., Karasu, G., & Yeşilipek, A. (2021). Pearson syndrome in a child transplanted for Diamond-Blackfan anemia. Síndrome de Pearson en un niño trasplantado debido a anemia de Diamond-Blackfan. Archivos argentinos de pediatria, 119(5), e559–e561. https://doi.org/10.5546/aap.2021.eng.e559en_US
dc.identifier.doi10.5546/aap.2021.eng.e559en_US
dc.identifier.endpage561en_US
dc.identifier.issue5en_US
dc.identifier.pmid34569763en_US
dc.identifier.scopus2-s2.0-85117616680en_US
dc.identifier.scopusqualityN/Aen_US
dc.identifier.startpage559en_US
dc.identifier.urihttps://doi.org/10.5546/aap.2021.eng.e559
dc.identifier.urihttps://hdl.handle.net/20.500.12713/2112
dc.identifier.volume119en_US
dc.identifier.wosWOS:000704188400032en_US
dc.identifier.wosqualityQ4en_US
dc.indekslendigikaynakWeb of Scienceen_US
dc.indekslendigikaynakScopusen_US
dc.indekslendigikaynakPubMeden_US
dc.institutionauthorUygun, Vedat
dc.institutionauthorDaloğlu, Hayriye
dc.language.isoenen_US
dc.publisherSociedad Argentina de Pediatriaen_US
dc.relation.ispartofArch Argent Pediatr .en_US
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/openAccessen_US
dc.subjectDiamond-Blackfan Anemiaen_US
dc.subjectPearson Syndromeen_US
dc.subjectHematopoietic Stem Cell Transplantation (HSCT)en_US
dc.subjectSociedad Argentina de Pediatríaen_US
dc.titlePearson syndrome in a child transplanted for diamond-blackfan anemiaen_US
dc.typeArticleen_US

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